Publications (23) María Ángeles Rodríguez Hernández publications

2017

  1. Role of p63 and p73 isoforms on the cell death in patients with hepatocellular carcinoma submitted to orthotopic liver transplantation

    PLoS ONE, Vol. 12, Núm. 3

2016

  1. Antitumoral gene-based strategy involving nitric oxide synthase type III overexpression in hepatocellular carcinoma

    Gene Therapy, Vol. 23, Núm. 1, pp. 67-77

  2. Free-thiamine is a potential biomarker of Thiamine transporter-2 deficiency: A treatable cause of Leigh syndrome

    Brain, Vol. 139, Núm. 1, pp. 31-38

  3. Regulation of apoptosis and cell proliferation by Sorafenib in Hepatocellular carcinoma

    Biosaia: Revista de los másteres de Biotecnología Sanitaria y Biotecnología Ambiental, Industrial y Alimentaria, Núm. 5

  4. Severe encephalopathy associated to pyruvate dehydrogenase mutations and unbalanced coenzyme Q 10 content

    European Journal of Human Genetics, Vol. 24, Núm. 3, pp. 367-372

  5. The CoQH2/CoQ Ratio Serves as a Sensor of Respiratory Chain Efficiency

    Cell Reports, Vol. 15, Núm. 1, pp. 197-209

2015

  1. Nitric Oxide Synthase Type III Overexpression By Gene Therapy Exerts Antitumoral Activity In Mouse Hepatocellular Carcinoma

    Redox biology, Vol. 5, pp. 420-421

  2. Primary coenzyme Q 10 deficiency presenting as fatal neonatal multiorgan failure

    European Journal of Human Genetics, Vol. 23, Núm. 9, pp. 1254-1258

  3. Regulation of cell death receptor S-nitrosylation and apoptotic signaling by Sorafenib in hepatoblastoma cells

    Redox Biology, Vol. 6, pp. 174-182

  4. Regulation of cell death signaling by nitric oxide in cancer cells

    Nitric Oxide and Cancer: Pathogenesis and Therapy (Springer International Publishing), pp. 247-258

2014

  1. Mitophagy Plays a Protective Role in Fibroblasts from Patients with Coenzyme Q10 Deficiency

    Autophagy: Cancer, Other Pathologies, Inflammation, Immunity, Infection, and Aging (Elsevier Inc.), pp. 131-144

2013

  1. Supercomplex assembly determines electron flux in the mitochondrial electron transport chain

    Science, Vol. 340, Núm. 6140, pp. 1567-1570

2012

  1. Haploinsufficiency of COQ4 causes coenzyme Q10 deficiency

    Journal of Medical Genetics, Vol. 49, Núm. 3, pp. 187-191

2011

  1. Apoptotic microtubule network organization and maintenance depend on high cellular ATP levels and energized mitochondria

    Apoptosis, Vol. 16, Núm. 4, pp. 404-424

  2. Secondary coenzyme Q 10 deficiency triggers mitochondria degradation by mitophagy in MELAS fibroblasts

    FASEB Journal, Vol. 25, Núm. 8, pp. 2669-2687

2009

  1. Coenzyme Q deficiency triggers mitochondria degradation by mitophagy

    Autophagy, Vol. 5, Núm. 1, pp. 19-32

  2. Coenzyme Q10 and alpha-tocopherol protect against amitriptyline toxicity

    Toxicology and Applied Pharmacology, Vol. 235, Núm. 3, pp. 329-337

2008

  1. Analysis of Coenzyme Q10 in muscle and fibroblasts for the diagnosis of CoQ10 deficiency syndromes

    Clinical Biochemistry, Vol. 41, Núm. 9, pp. 697-700

2007

  1. Missense mutation of the COQ2 gene causes defects of bioenergetics and de novo pyrimidine synthesis

    Human Molecular Genetics, Vol. 16, Núm. 9, pp. 1091-1097

  2. The apoptotic microtubule network preserves plasma membrane integrity during the execution phase of apoptosis

    Apoptosis, Vol. 12, Núm. 7, pp. 1195-1208